About a Rare Case of Low-Grade Chondrosarcoma of the Cranial Vault


  • Leonello Tacconi Unita’ di Neurochirurgia, Azienda Universitaria Integrata, Trieste, Italia
  • Gennaro D’Acunzi U.O.C. Neurochirurgia, P.O. “Umberto I” ” - Nocera Inferiore-Pagani, Plesso di Nocera Inferiore, ASL Salerno, Italy
  • Camilla Russo Dipartimento di Scienze Biomediche Avanzate, Università degli Studi di Napoli “Federico II”, Napoli, Italy
  • Andrea Manto Servizio di Neuroradiologia, P.O. “Umberto I” - Nocera Inferiore-Pagani, Plesso di Nocera Inferiore, ASL Salerno, Italy
  • Ginevra F. D’Onofrio U.O.C. Neurochirurgia, P.O. “Umberto I” ” - Nocera Inferiore-Pagani, Plesso di Nocera Inferiore, ASL Salerno, Italy
  • Raffaele Fristachi Servizio di Anatomia Patologica, D.E.A. Nocera Inferiore-Pagani, Plesso di Pagani, ASL Salerno, Italy




Chondrosarcoma, Computed Tomography, Magnetic Resonance Imaging, skull base, malignant tumor, adjuvant radiotherapy.


Chondrosarcoma is a rare malignant tumour arising from the cartilage with a high variability in the clinicalcourse and overall prognosis. This entity has, generally, a predilection for long bones of the limbs and pelvis and the location in the cranial bones is quite rare. We report a case of a 38 year male with a large and poorly symptomatic parafalcine chondrosarcoma of the cranial vault which was removed en bloc. The described location is extremely rare.

Magnetic Resonance Imaging permitted to better delineate the lesion and plan the most appropriate therapeutic approach. Final diagnosis was based on histological examination, which confirmed the hypothesis of low-grade parafalcine chondrosarcoma. Even though surgery remains the mainstay of treatment for cerebral chondrosarcomas, adjuvant radiotherapy such as stereotactic, proton beam or carbon ion-beam therapy might be necessary in aggressive or incomplete removed cases.


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How to Cite

Leonello Tacconi, Gennaro D’Acunzi, Camilla Russo, Andrea Manto, Ginevra F. D’Onofrio, & Raffaele Fristachi. (2018). About a Rare Case of Low-Grade Chondrosarcoma of the Cranial Vault . Journal of Cancer Research Updates, 7(1), 35–40. https://doi.org/10.6000/1929-2279.2018.07.02.1